Clinical review (n = 45) [9, 11,12,13, 15,16,17,18, 21,22,23, 26,27,28,29,30,31,32,33,34,35,36,37,38,39,40,41,42,43,44,45,46,47,48] | Percentage (number of cases) |
---|---|
Gender | |
Male | 60% (27) |
Female | 40% (18) |
Type | |
Unilateral | 44.5% (20) |
Bilateral | 20% (9) |
Complex | 29% (13) |
Unreported | 6.5% (3) |
Mean age | |
Overall | 28 months (1 week–16 years) |
Unilateral | 46 months (3 weeks–16 years) |
Bilateral | 14 months (1 week–6 years) |
Complex | 12.5 months (2 months–6 years) |
Symptoms | |
Upper GI bleeding | 63% (28) |
Failure to thrive | 53.5% (24) |
Diarrhea or steatorrhea | 42.2% (19) |
Vomiting | 18% (8) |
Signs | |
Splenomegaly | 54% (24) |
Ascites or edema | 51% (23) |
Abdominal distension | 36% (16) |
Hepatomegaly | 33.5% (15) |
Right upper quadrant bruit | 36% (16) |
Laboratory | |
Anemia | 73.5% (33) |