Scrotoschisis: a case report
© The Author(s). 2017
Received: 18 May 2017
Accepted: 16 August 2017
Published: 13 September 2017
Scrotoschisis is a rare congenital anomaly of the scrotal wall with idiopathic etiology and unknown prevalence. This pathology is extremely rare. We report a new case and review the literature for relevant data.
A 3-day-old full-term baby boy of African ethnicity, who had a homebirth, with birth weight of 2.7 kg presented to our emergency department with exteriorization of left testis; after clinical examination and proper investigations the diagnosis was scrotoschisis. Surgical treatment was performed by primary closure with excellent follow-up. We reviewed the literature to elaborate on the etiology of this pathology and its management.
Scrotoschisis is a rare congenital anomaly affecting healthy babies. Early management is substantial. Further studies are recommended to learn more about the etiology and long-term results, including the effect on the fertility.
KeywordsTesticular exstrophy Scrotal wall abnormality Orchidopexy
Scrotoschisis is a rare congenital anomaly of the scrotal wall with idiopathic etiology and unknown prevalence. This pathology is extremely rare. In this anomaly, the testis eviscerates through an opening high on the anterior wall of the scrotum . The exact birth prevalence of scrotoschisis is unknown. We report the 17th case in the literature. In this case report, we highlighted etiology hypotheses and management considerations.
Scrotoschisis is a rare congenital scrotal wall pathology. Its prevalence is unknown. Only 16 cases were reported in the literature [2, 3]. It is a semi-urgent condition which should be managed immediately if it presents with a testicular torsion. There are many hypotheses for its etiology: Failure of differentiation of scrotal mesenchyme layer results in rupture or avascular necrosis of overlying epithelium leading to scrotal wall defect . Other reports mentioned external mechanical compression effect due to arthrogryposis , as well as meconium periorchitis . In our case, we have no obvious cause; there is no evidence of meconium residua and neither is there evidence of traumatism. Iatrogenic injury is a potential cause and could be concurrently associated if obstetrical difficulties were encountered during labor, mostly if completed by cesarean section . Broad-spectrum antibiotics should be commenced immediately on diagnosis. During a physical examination, it is fundamental to rule out testicular torsion (due to lack of testicular anatomical attachments). A local aseptic dressing procedure is imperative to avoid possible orchitis or peritonitis in case of communicating patent processus vaginalis. A surgical approach depends on the severity and could be a simple dressing with healing by secondary intention  or conventional surgical method in two planes horizontally or vertically after orchidopexy. In our case, we preferred to close in two layers horizontally; the skin defect was mainly horizontal. Postoperative follow-up should not be discontinued until verification of two symmetric, vital, and normally growing testes. Further research is recommended to study the effect of scrotoschisis on fertility.
Scrotoschisis is a rare congenital anomaly affecting otherwise healthy babies. Early management is substantial. Further studies are recommended to learn more about the etiology and long-term results, including fertility.
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No data sets were generated or analyzed during this study.
SS managed the case, collected and evaluated the data; MC assisted in managing the case and did the first draft of manuscript; SG received and critically revised the manuscript and coordinated the submission; and all authors read and approved the final manuscript.
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