Skip to main content

Table 1 Summary of recorded physiology

From: Successful pregnancy in pulmonary arterial hypertension associated with systemic lupus erythematosus: a case report

    Pregnancy  
  Diagnosis PAH 3 months later 5th week 20th week 35th week Delivery 3 months postpartum
NYHA IV III III III III III IV
6-MWT m 229 423 454 396 276   392
RVSP mmHg (Echo) 69   normal normal 40   57
SPAP mmHg 72 57     45  
MPAP mmHg 52 35     21  
PAOP mmHg 10 8     7  
CI L/min/m2 1.3 3.4     4.3  
PVR dyn.sec.cm−5 1580 410     250  
mVO2% 35 67     69  
SLEDAI [14] 17 2 2    14 18
Phenprocoumon (INR)   2.1 2.2     2.1
LMWH (Dalteparin E/day)     10,000 10,000   
Prednisone (mg/day) 50 30 10 25 25 50 50
Hydroxychloroquine (mg/day) 200 200 200 200 200 200 200
Cyclophosphamide (mg/day) 100 100      
Azathioprine (mg/day)    100 100 100 100 150
Bosentan (mg/day) 250 250      250
Sildenafil (mg/day) 150 150 150 150 150 150 150
Inhaled iloprost (μg/day)      50 100  
  1. NYHA, New York Heart Association; 6-MWT, 6 minute walking test distance; RVSP, echocardiographic systolic right ventricular pressure over right atrial pressure; hemodynamic assessments by right heart catheterization: SPAP, systolic pulmonary arterial pressure; MPAP, mean pulmonary arterial pressure; PAOP, pulmonary arterial occlusive pressure; CI, cardiac index; PVR, pulmonary vascular resistance; mVO2, mixed venous oxygen saturation; SLEDAI, systemic lupus erythematosus disease activity index; LMWH, low molecular weight heparin.