|  |  | Pregnancy |  | |||
---|---|---|---|---|---|---|---|
 | Diagnosis PAH | 3 months later | 5th week | 20th week | 35th week | Delivery | 3 months postpartum |
NYHA | IV | III | III | III | III | III | IV |
6-MWT m | 229 | 423 | 454 | 396 | 276 | Â | 392 |
RVSP mmHg (Echo) | 69 | Â | normal | normal | 40 | Â | 57 |
SPAP mmHg | 72 | 57 | Â | Â | Â | 45 | Â |
MPAP mmHg | 52 | 35 | Â | Â | Â | 21 | Â |
PAOP mmHg | 10 | 8 | Â | Â | Â | 7 | Â |
CI L/min/m2 | 1.3 | 3.4 | Â | Â | Â | 4.3 | Â |
PVR dyn.sec.cm−5 | 1580 | 410 |  |  |  | 250 |  |
mVO2% | 35 | 67 | Â | Â | Â | 69 | Â |
SLEDAI [14] | 17 | 2 | 2 | Â | Â | 14 | 18 |
Phenprocoumon (INR) | Â | 2.1 | 2.2 | Â | Â | Â | 2.1 |
LMWH (Dalteparin E/day) | Â | Â | Â | 10,000 | 10,000 | Â | Â |
Prednisone (mg/day) | 50 | 30 | 10 | 25 | 25 | 50 | 50 |
Hydroxychloroquine (mg/day) | 200 | 200 | 200 | 200 | 200 | 200 | 200 |
Cyclophosphamide (mg/day) | 100 | 100 | Â | Â | Â | Â | Â |
Azathioprine (mg/day) | Â | Â | 100 | 100 | 100 | 100 | 150 |
Bosentan (mg/day) | 250 | 250 | Â | Â | Â | Â | 250 |
Sildenafil (mg/day) | 150 | 150 | 150 | 150 | 150 | 150 | 150 |
Inhaled iloprost (μg/day) |  |  |  |  | 50 | 100 |  |