Table 2 Diagnostic criteria of familial Mediterranean fever adapted from Livneh et al.

Major criteria

Typical attacks

(1) Peritonitis (generalized)

(2) Pleuritis (unilateral) or pericarditis

(3) Monoarthritis (hip, knee, ankle)

(4) Fever (rectal temperature 38 °C or higher, lasting between 12 h and 3 days)

Minor criteria

(1) Incomplete attacks involving one or more of the following sites: (a) Abdomen (localized, no signs of peritonitis) or (b) chest

(2) Joint (arthritis involving other joints)

(3) Exertional leg pain

(4) Favorable response to colchicine