Large vessel vasculitis |
 Takayasu arteritis |
 Giant cell arteritis |
Medium vessel vasculitis |
 Polyarteritis nodosa |
 Kawasaki disease |
Small vessel vasculitis |
 ANCA-associated vasculitis • Microscopic polyangiitis • Granulomatosis with polyangiitis (Wegener’s) • Eosinophilic granulomatosis with polyangiitis (Churg Strauss) |
 Immune complex small vessel vasculitis • Antiglomerular basement membrane disease • Cryoglobulinemic vasculitis • IgA vasculitis (Henoch-Schönlein) • Hypocomplementemic urticarial vasculitis |
Variable vessel vasculitis |
 Behcet’s disease |
 Cogan’s syndrome |
Single-organ vasculitis |
 Cutaneous leukocytoclastic angiitis |
 Cutaneous arteritis |
 Primary central nervous system vasculitis |
 Isolated aortitis |
 Others |
Vasculitis associated with systemic disease |
Lupus vasculitis |
Rheumatoid vasculitis |
Sarcoid vasculitis |
Others |
Vasculitis associated with probable etiology |
Hepatitis C virus-associated cryoglobulinemic vasculitis |
Hepatitis B virus-associated vasculitis |
Syphilis-associated aortitis |
Drug-associated immune complex vasculitis |
Drug-associated ANCA-associated vasculitis |
Cancer-associated vasculitis |
 Others |