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Table 1 Names for vasculitides adopted by the 2012 International Chapel Hill Consensus Conference on the Nomenclature of Vasculitides [2]

From: Refractory drug-induced systemic small-vessel vasculitis with two varied extracutaneous manifestations: a case report and review of the literature

Large vessel vasculitis

 Takayasu arteritis

 Giant cell arteritis

Medium vessel vasculitis

 Polyarteritis nodosa

 Kawasaki disease

Small vessel vasculitis

 ANCA-associated vasculitis

• Microscopic polyangiitis

• Granulomatosis with polyangiitis (Wegener’s)

• Eosinophilic granulomatosis with polyangiitis (Churg Strauss)

 Immune complex small vessel vasculitis

• Antiglomerular basement membrane disease

• Cryoglobulinemic vasculitis

• IgA vasculitis (Henoch-Schönlein)

• Hypocomplementemic urticarial vasculitis

Variable vessel vasculitis

 Behcet’s disease

 Cogan’s syndrome

Single-organ vasculitis

 Cutaneous leukocytoclastic angiitis

 Cutaneous arteritis

 Primary central nervous system vasculitis

 Isolated aortitis

 Others

Vasculitis associated with systemic disease

Lupus vasculitis

Rheumatoid vasculitis

Sarcoid vasculitis

Others

Vasculitis associated with probable etiology

Hepatitis C virus-associated cryoglobulinemic vasculitis

Hepatitis B virus-associated vasculitis

Syphilis-associated aortitis

Drug-associated immune complex vasculitis

Drug-associated ANCA-associated vasculitis

Cancer-associated vasculitis

 Others