Fig. 2

Fundus examination showed diffuse loss of the nerve fiber layer and an excavated optic nerve head with advanced-stage glaucoma. The red, sunset-like fundus around the optic disc was seen due to a lack of pigmentation in the RPE layer. A normal retinal appearance can be seen in the area two or three optic disc distances away from the optic disc. Posterior segmental OCT showed abnormal retina with thinning of choroidal tissue at the parafovea in the left eye. a Fundus photograph of the right eye; b Fundus photograph of the left eye; c Macular image with OCT of the right eye; d Macular image with OCT of the left eye