From: Vascular thromboses with retroperitoneal fibrosis: a case report
Diagnostic criteria | Arguments |
---|---|
Clinical | Lung: chest pain with hemoptoic sputum, bilateral nodular excavated lung lesions Kidney: microscopic hematuria, positive urine sediment, 24-hour proteinuria ENT: dysphonia, epistaxis, left ear deafness, subglottic stenosis on nasofibroscopy, perforation of the medial sinus wall Ophthalmic: red eyes, bilateral episcleritis Cardiovascular involvement: multiple thrombosis, circumferential pericardial effusion Lumbar: lumbago, retroperitoneal fibrosis |
Biology | Anticytoplasmic neutrophil antibodies ANCA-PR3 positive at 63Â IU/mL |
Histology | Biopsies not done because of the therapeutic emergency and the impossibility of stopping the anticoagulant treatment |