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Table 2 Clinical characteristics of two cases

From: Hereditary pheochromocytoma/paraganglioma syndrome with a novel mutation in the succinate dehydrogenase subunit B gene in a Japanese family: two case reports

 

Daughter

Father

Sex

Female

Male

Age at diagnosis

19

40

Primary tumor size

5 × 4 × 2.5 cm

10 × 7 × 4 cm

Primary tumor localization

Abdominal PGL

Abdominal PGL

Catecholamine type

Noradrenaline type

Nonfunctioning type

Metastasis

No metastasis

Rib, liver, pleura

Ki-67 index

5.10%

1.50%

GAPP score

6 (moderately differentiated)

3 (moderately differentiated)

  1. PGL, paraganglioma; GAPP, grading system for adrenal pheochromocytoma and paraganglioma