From: Congenital absence of lingual frenum in a non-syndromic patient: a case report
Systemic criteria | • Skin involvement ◦ Hyperextensibility of skin ◦ Translucent skin ◦ Atrophic “cigarette paper” ◦ Skin scarring ◦ Subcutaneous nodules • Joint hypermobility • Cicatrization disorders • Easy bruising • Eyelid extensibility (Metenier’s sign) • Pseudotumors • Postural acrocyanosis |
Temporomandibular joint and intra-oral criteria | • Recurrent subluxation of the temporomandibular joint • Tongue hypermobility (Gorlin’s sign) • Absence of lingual frenulum |