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Table 2 Common clinical features associated with Ehlers–Danlos syndromes [10, 12]

From: Congenital absence of lingual frenum in a non-syndromic patient: a case report

Systemic criteria

• Skin involvement

 ◦ Hyperextensibility of skin

 ◦ Translucent skin

 ◦ Atrophic “cigarette paper”

 ◦ Skin scarring

 ◦ Subcutaneous nodules

• Joint hypermobility

• Cicatrization disorders

• Easy bruising

• Eyelid extensibility (Metenier’s sign)

• Pseudotumors

• Postural acrocyanosis

Temporomandibular joint and intra-oral criteria

• Recurrent subluxation of the temporomandibular joint

• Tongue hypermobility (Gorlin’s sign)

• Absence of lingual frenulum