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Table 2 Application of Yamaguchi clinical criteria in presented patient

From: Noncaseating suppurative granulomatous lymphadenitis in adult onset Still’s disease – a diagnostic dilemma in a tuberculosis-endemic region: a case report

Yamaguchi criteria

Patient’s characteristics

Major Yamaguchi criteria

 Fever of at least 39 °C lasting at least 1 week

+

 Arthralgias or arthritis lasting 2 weeks or longer

+

 Typical rash (maculopapular, nonpruritic) during febrile episodes

 Leukocytosis (10,000/μL or greater) with at least 80% granulocytes

Minor Yamaguchi criteria

 Sore throat

 Lymphadenopathy

+

 Hepatomegaly or splenomegaly

 Abnormal liver function studies

+

 Negative antinuclear antibodies and rheumatoid factor

+

Exclusions

 Infection

Done

 Malignancies: mainly lymphoproliferative

Done

 Other rheumatological disorders

Done

  1. Yamaguchi criteria require the presence of five features, with at least two being major diagnostic criteria