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Table 2 Reported cases of composite pheochromocytoma/paragangliomas associated with MEN 2A/B

From: Bilateral pheochromocytoma with ganglioneuroma component associated with multiple neuroendocrine neoplasia type 2A: a case report

Age(years)/sex

MEN type

Tumor size/weight

Organ

Neurogenic component

Outcome

Reference/country/year

34/M

2A

1.6 cm/11,8g

Left adrenal medulla

Ganglioneuroma

Uneventful postoperative course

Brady et al. [6]/USA/1997

49/M

2A

600g

Left adrenal medulla

Ganglioneuroblastoma

Died after orthopedic surgery (postmortem incidental finding)

Matias-Guiu et al. [7]/Spain/1998

27/F

2B

10 cm/124g

Left adrenal medulla

Ganglioneuroma

Tumor free for 16 months after surgery

Charfi et al. [8]/Tunisia/2008

59/M

2B

3 cm

Retroperitoneum

Ganglioneuroma

Metastatic disease at diagnosis

Yamasaki et al. [9]/Japan/2016

40/F

2A

9 cm

Right adrenal medulla

Ganglioneuroma

Tumor free for 3 years

Our case/Morocco

  1. MEN2A/2B multiple endocrine neoplasia type 2A or 2B, M Male, F Female