From: Papillon–Lefèvre syndrome: a series of five cases among siblings
Variables | Cases | |||||
---|---|---|---|---|---|---|
1 | 2 | 3 | 4 | 5 | ||
Gender | F | M | M | M | M | |
Age (years) | 3 | 4 | 11 | 12 | 14 | |
Periodontal manifestations | Gingivitis | + | + | + | + | + |
Periodontitis; Basic Periodontal Examination (BPE) Score | 4 | 4 | 4 | 4 | 4 | |
Primary teeth loss | + | + | + | + | + | |
Permanent teeth loss | – | – | – | + | + | |
Alveolar bone resorption | + | + | + | + | + | |
Halitosis | + | + | + | + | + | |
Skin manifestations | Palmoplantar hyperkeratosis | – | + | + | + | + |
Elbows | + | + | + | + | + | |
Knees | + | + | + | – | + | |
Toes | + | + | + | – | – | |
Dorsal fingers | – | – | + | + | – |