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Table 1 Reported cases of the acute phase of idiopathic systemic capillary leak syndrome

From: A fatal case of acute progression of generalized edema and simultaneous flash pulmonary edema in a patient with idiopathic systemic capillary leak syndrome: a case report

Case (reference)

Age (yrs)

Sex

SBP (mmHg)

HR (beats/min)

TP / Alb (g/dL)

Ht / Hb (g/dL)

Pulmonary edema

Intubation

Treatment

Outcome

1 [2]

46

M

56

96

4.3/2.5

61.7% / 21.9

+ (day 2, R.P.)

+(day 3)

Saline: 10L/12hr, Alb

A

2 [7]

49

F

Shock

Shock

None

None

-

-

Saline

A

3 [7]

54

M

Shock

Shock

3.7 / None

56% / None

-

-

Saline: 4.5L+Alb

A

4 [7]

44

F

Shock

Shock

None

None

-

-

None

A

5 [8]

24

M

80

130

5.5 / 3.0

None / 12

-

-

Saline: 1L+0.5L/hr+C

A

6 [10]

52

F

Shock

Shock

None

67% / None

+(R.P.)

-

Plasma expander: 1500mL/24hrs

A

7 [11]

53

M

Shock

100

None / 1.3

67% / None

-

-

Saline: 2L+3L/48hr

A

8 [12]

38

F

80

None

4.4 / None

49.9% / 16.8

-

-

Saline: 4.5L+Alb+C

A

9 [13]

37

F

40

110

None

53% / 19.2

+(day 1)

+

Saline:9L+10% P+S0.5L/hr+C

A

10 [13]

36

F

40

130

4.4 / None

49.9% / 16.8

-

-

10% P+S

A

11 [14]

41

M

70

40

None / 1.8

None / 22.5

+(day 3, R.P.)

+

Saline: 15L, Alb+C

A

12 [15]

41

M

65

102

2.3 / none

60.4% / 22.3

-

+

Saline: 15L+Nad

A

13 [16]

62

F

97

None

None

None / 19.7

+ (day 5)

+ (day 5)

Saline+C+IMG+S

D (day 9)

  1. SBP, systolic blood pressure; HR, heart rate; TP, total protein; Alb, albumin; Ht, hematocrit; Hb, hemoglobin; F, female; M, male; None, data not described; R.P., recruitment phase; C, catecholamine; P, pentastarch; S, steroid; Nad, noradrenaline; IMG, immunoglobulins; A, alive; D, death.