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Table 2 Classification of HLH

From: Hemophagocytic lymphohistiocytosis and miliary tuberculosis in a previously healthy individual: a case report

Primary HLH

Secondary HLH

Malignant

Nonmalignant

Hematological malignancies

Solid tumors

Autoimmune

Infectious

Genetic defects impairing NK and T cell function

Lymphoma

Acute leukemias

MDS

Lung

GI tract

Pancreas

UG tract

SLE

Still’s disease

Rheumatoid arthritis

EBV

Leishmania

CMV

SARS-CoV-2

HIV

Protozoa

Fungal infections

TB

  1. MDS myelodysplastic syndrome, GI tract gastrointestinal tract, UG tract urogenital tract SLE systemic lupus erythematosus, EBV Epstein–Barr virus, CMV cytomegalovirus, HIV human immunodeficiency virus, TB tuberculosis