Fig. 1

Ammonia (μmol/L) and hemoglobin (g/dL) levels in a 48-year-old man with hyperornithinemia-hyperammonemia-homocitrullinuria syndrome during an acute episode of hyperammonemia. Days from admission are presented on the x-axis. The diagnosis was suspected on day 2 and active treatment started. Initiation of treatment with scavenger (sodium benzoate) and duration of continuous renal replacement therapy is illustrated as well as erythrocyte transfusions