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Table 1 Characteristics of patients diagnosed with frosted branch angiitis as an ocular manifestation of Behçet’s disease

From: Frosted branch angiitis and cerebral venous sinus thrombosis as an initial onset of neuro-Behçet’s disease: a case report and review of the literature

Authors, year [reference]

Country

Past history

Laterality

Initial BCVA (OD/OS)

Final BCVA (OD/OS)

HLA-B51

Hypopyon

Neuro-Behçet disease

Reynders et al., 2005 [6]

Belgium

OrU, GU, skin lesions

OU

20/400, CF

20/40, 20/200

+

(−)

(−)

Renard et al., 2009 [23]

France

OrU, skin lesions

OD

20/200

20/20

+

(−)

(−)

Jackson et al., 2011 [24]

United Kingdom

OrU, GU, skin lesions

OS

HM

20/60

+

(−)

(−)

Ramachandran et al., 2011 [22]

United Kingdom

OrU, GU

OU

NA

a

(−)

+

+

Al-Mujaini et al., 2011 [7]

Oman

OrU, GU, skin lesions

OUb

20/100, NA

a

NA

(−)

+

Portero et al., 2011 [5]

Spain

OrU, skin lesions

OU

20/200, 20/120

20/20, 20/20

+

(−)

+

Kwon et al. 2012 [26]

Korea

OrU, GU

OS

HM

HM

+

+

(−)

Kumar et al., 2015 [25]

India

None

OD

LP

20/60

+

(−)

(−)

Schwatz et al., 2016 [27]

Israel

OrU, GU, skin lesions

OD

20/100

20/22

+

(−)

+

Present case

Brazil

OrU, headache

OU

HM, HM

CF, 20/130

(−)

(−)

+

  1. Abbreviations: BCVA Best corrected visual acuity, OrU Oral ulcers, GU Genital ulcers, OU Both eyes, OD Right eye, OS Left eye, CF Counting fingers, HM Hand movement, LP light perception, NA Not available, HLA Human leukocyte antigen
  2. aDescribed as clinical improvement
  3. bTwo years apart