From: Granulomatosis with polyangiitis (Wegener’s) as a necrotizing gingivitis mimic: a case report
Site | Presentations | Frequency of disease occurrence at site throughout disease course (%) |
---|---|---|
Oral or nasal ulcers, strawberry gums, strawberry tongue, unresponsive upper respiratory tract or ear ‘infections’ , otitis, vestibular nerve injury, conductive or sensorineural deafness | 92 | |
Subglottic stenosis, pulmonary nodular infiltrates, pulmonary hemorrhage ‘ground-glass’ infiltrations, pleurisy | 85 | |
Rapidly progressing glomerulonephritis - necrotizing | 80 | |
Myalgias, migratory pauciarticular or polyarticular arthritis, arthralgias | 67 | |
Scleritis, episcleritis, orbital pseudotumor, proptosis, dacrocystis | 52 | |
Palpable purpura, ulcers, leucocytoclastic vasculitis, subcutaneous nodules, gangrene | 46 | |
Peripheral neuropathy, mononeuritis multiplex, cranial neuropathy, meningitis | 20 | |
Myocarditis, pericarditis, cerebral vasculitis, mass lesions (brain, renal, lung, orbit, breast, prostate, ovary, parotid) |