From: Fulminant systemic capillary leak syndrome due to C1 inhibitor deficiency complicating acute dermatomyositis: a case report
Parameter
Normal range
C3 Complement
14mg/dL
86–184mg/dL
C4 Complement
<6mg/dL
10–40mg/dL
C1 Inhibitor
18–32mg/dL
C1 Inhibitor activity
34%
70–130%