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Table 1 Cognition and neuromuscular status – amyotrophy in prion disease

From: A patient with Creutzfeldt-Jakob disease presenting with amyotrophy: a case report

 

Hospital day

 

Day 1

Day 7

Day 10

Day 16

Day 30

Cognition:

     

Mini mental state examination

25

-

23

9

0

Clock drawing test

4

-

3

0

0

Total functional capacity

12

-

2

1

0

Addenbrooke’s cognitive assessment (revised)

83

-

72

38

0

• Attention and orientation

16/18

-

13/18

4/18

0

• Memory

22/26

-

20/26

13/26

0

• Fluency

10/14

-

8/14

8/14

0

• Language

22/26

-

20/26

13/26

0

Visuospatial

13/16

-

11/16

0/16

0

Neuromuscular:

     

Neck

F

5*

5

4

3

2

 

E

5

5

4

3

2

Hip

F

4(L), 5(R)

3(L), 3(R)

3(L), 3(R)

3(L), 3(R)

2(L), 2(R)

 

E

4, 5

3, 3

3, 3

3, 3

2, 2

Hip

ABD

4, 5

3, 4

3, 3

3, 3

2, 2

 

ADD

4, 5

3, 4

3, 3

3, 3

2, 2

Knee

F

4, 5

3, 3

3, 3

3, 3

2, 2

 

E

4, 5

3, 3

3, 3

3, 3

2, 2

Ankle

DF

5, 5

3, 3

3, 3

3, 3

2, 2

 

PF

5, 5

4, 4

3, 3

3, 3

2, 2

 

INV

5, 5

3, 3

2, 2

2, 2

2, 2

 

EV

5, 5

3, 3

2, 2

2, 2

2, 2

Shoulder

ABD

5, 5

5, 5

4, 4

3, 3

2, 2

 

F

5, 5

5, 5

4, 4

3, 3

2, 2

 

E

5, 5

5, 5

4, 4

3, 3

2, 2

Elbow

F

5, 5

5, 5

3, 3

3, 3

2, 2

 

E

5, 5

5, 5

3, 3

3, 3

2, 2

Wrist

F

5, 5

5, 5

3, 3

3, 3

2, 2

 

E

5, 5

5, 5

3, 3

3, 3

2, 2

Finger

F

5, 5

5, 5

3, 3

3, 3

2, 2

 

E

5, 5

5, 5

3, 3

3, 3

2, 2

  1. *Medical Research Council Scale 0 to 5. F Flexion, E Extension, ABD Abduction, ADD Adduction, PF Plantar flexion, INV Inversion, EV Eversion, DF Dorsiflexion, L Left, R Right.