From: A patient with Creutzfeldt-Jakob disease presenting with amyotrophy: a case report
 | Hospital day | |||||
---|---|---|---|---|---|---|
 | Day 1 | Day 7 | Day 10 | Day 16 | Day 30 | |
Cognition: | Â | Â | Â | Â | Â | |
Mini mental state examination | 25 | - | 23 | 9 | 0 | |
Clock drawing test | 4 | - | 3 | 0 | 0 | |
Total functional capacity | 12 | - | 2 | 1 | 0 | |
Addenbrooke’s cognitive assessment (revised) | 83 | - | 72 | 38 | 0 | |
• Attention and orientation | 16/18 | - | 13/18 | 4/18 | 0 | |
• Memory | 22/26 | - | 20/26 | 13/26 | 0 | |
• Fluency | 10/14 | - | 8/14 | 8/14 | 0 | |
• Language | 22/26 | - | 20/26 | 13/26 | 0 | |
Visuospatial | 13/16 | - | 11/16 | 0/16 | 0 | |
Neuromuscular: | Â | Â | Â | Â | Â | |
Neck | F | 5* | 5 | 4 | 3 | 2 |
 | E | 5 | 5 | 4 | 3 | 2 |
Hip | F | 4(L), 5(R) | 3(L), 3(R) | 3(L), 3(R) | 3(L), 3(R) | 2(L), 2(R) |
 | E | 4, 5 | 3, 3 | 3, 3 | 3, 3 | 2, 2 |
Hip | ABD | 4, 5 | 3, 4 | 3, 3 | 3, 3 | 2, 2 |
 | ADD | 4, 5 | 3, 4 | 3, 3 | 3, 3 | 2, 2 |
Knee | F | 4, 5 | 3, 3 | 3, 3 | 3, 3 | 2, 2 |
 | E | 4, 5 | 3, 3 | 3, 3 | 3, 3 | 2, 2 |
Ankle | DF | 5, 5 | 3, 3 | 3, 3 | 3, 3 | 2, 2 |
 | PF | 5, 5 | 4, 4 | 3, 3 | 3, 3 | 2, 2 |
 | INV | 5, 5 | 3, 3 | 2, 2 | 2, 2 | 2, 2 |
 | EV | 5, 5 | 3, 3 | 2, 2 | 2, 2 | 2, 2 |
Shoulder | ABD | 5, 5 | 5, 5 | 4, 4 | 3, 3 | 2, 2 |
 | F | 5, 5 | 5, 5 | 4, 4 | 3, 3 | 2, 2 |
 | E | 5, 5 | 5, 5 | 4, 4 | 3, 3 | 2, 2 |
Elbow | F | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |
 | E | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |
Wrist | F | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |
 | E | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |
Finger | F | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |
 | E | 5, 5 | 5, 5 | 3, 3 | 3, 3 | 2, 2 |