Reference | Cystic fibrosis genotype | Cystic fibrosis complications | Hemoglobin disease classification | Hematologic complications | Co-morbid conditions |
---|---|---|---|---|---|
Porter et al. [9] | Unknown | -Meconium ileus | Hemoglobin SS | -Acute transfusions | -None reported |
Porter et al. [9] | Unknown | -Recurrent bronchitis | Hemoglobin SS | -Anemia | -None reported |
Amendola et al. [10] | Unknown | -Recurrent bronchitis | Hemoglobin SD | -Chronic transfusions | -None reported |
-Pancreatic insufficiency | |||||
Warwick et al. [11] | Unknown | -Recurrent bronchitis | Hemoglobin SS | -Bone pain | -Cardiomegaly |
-Pancreatic insufficiency | |||||
Banjar [12] | H549L/S549R | -Sinusitis | Hemoglobin SS | -Bone pain | -Obstructive sleep apnea |
-Recurrent bronchitis | -Chronic transfusions | -Hypercalciuria | |||
-Pancreatic insufficiency | -Gastroesophageal reflux | ||||
Current case | C53+2T>C/Unknown | -Recurrent bronchitis | Hemoglobin-β+ thalassemia | -Bone pain | -Gastroesophageal reflux |
-Failure to thrive | -Abdominal sequestration | -Nissen fundoplication | |||
-Burkholderia cepacia | -Acute chest syndrome | -Gastrostomy tube | |||
-Pancreatic insufficiency | -Chronic transfusions | -Central line infections | |||
-Lactase deficiency | |||||
-Total parenteral nutrition |