Reference | Age / Sex | Years | Pathologic diagnosis | Neurological manifestation | Treatement | Outcome |
---|---|---|---|---|---|---|
Pirani and Bennet, 1951[1] | 22 Male | 16 | CP and systemic vasculitis | Depressed MS, seizures | NR | Exitus |
Sokoloff and Bunim, 1957[2] | 64 Male | 30 | CP and systemic vasculitis | NR | GC | Exitus |
Johnson et al. 1959[3] | 37 Female | 1 year 8 month | CP and systemic vasculitis | Seizures | GC | Exitus |
Johnson et al. 1959[3] | 63 Male | 3 | CP and systemic vasculitis | Hemiparesis | GC | Exitus |
Steiner and Gellbloom, 1959[4] | 62 Male | 20 | CP vasculitis | CN dysfunction, depressed MS | GC | Exitus |
Ouyang et al. 1967[5] | 58 Female | 30 | CP vasculitis | Seizures, hemiparesis | GC | Exitus |
Ramos and Mandybur, 1975[6] | 63 Male | 1 | CP and systemic vasculitis | Gerstmann syndrome | NR | Exitus |
Watson et al. 1977[7] | 54 Female | 20 | CP vasculitis | CN dysfunction, aphasia, hemiparesis, ataxia | GC | Exitus |
Kiss et al. 2006[8] | 51 Female | 39 | CP and systemic vasculitis | Hemiparesis | GC immunoglobulin | Exitus |
Rodriguez et al. 2006[9] | 49 Female | 10 | CP vascultis | Aphasia, hemianopia | GC cyclophosphamide | Improvement |
Rodriguez et al. 2006[9] | 70 Female | Recent diagnosis | CP vascultis | Seizures | GC cyclophosphamide | Improvement |
Mrabet et al. 2007[10] | 59 Female | 20 | CP vascultis | Headache, diplopia, and gait disorders | High-dose GC cyclophosphamide | Improvement |
Caballol Pons et al. 2010[11] | 71 Female | 15 | CP vascultis | Headache, dysarthria | High-dose GC | Improvement |
Ohno et al. 1994[12] | 46 Female | 16 | CP vasculitis | dysarthria and left hemiparesis | methotrexate therapy | Improvement |
Present case | 52 Female | 9 | CP vascultis | Headache | Intensification MTX therapy | Improvement |