Table 1 Patient’s characteristics and clinical manifestations, diagnostic findings and treatment
Patient’s characteristics and clinical manifestations | |
|---|---|
Sex | female |
Age (years) | 11 |
Prodromal symptoms | yes |
Symptom presentation | |
Behaviour/personality change | yes |
Seizures | yes |
Dystonia | yes |
Orolingual dyskinesias | yes |
Speech reduction | yes |
Dystonic postures | yes |
Muscle rigidity | yes |
Autonomic instability | yes (urinary incontinence) |
Central hypoventilation | no |
MRI-abnormal findings | no |
EEG-disorganized activity, focal or diffuse (non specific) | yes |
EEG-epileptic activity | no |
CSF-pleocytosis | yes (5WBC/μL) |
CSF protein concentration >45mg/dl | no |
CSF-oligoclonal bands | yes |
Tumor-ovarian teratoma | no |
Treatment | |
Supportive care | yes |
IVIG | yes |
Glucocorticosteroids | yes |
Cyclophosphamide | yes |
Outcome | |
Substantial improvement/Full recovery | yes |