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Table 1 Classification of non-infectious granulomatous lung diseases according to the distribution and the presence of necrosis

From: Multiple granulomatous lung lesions in a patient with Epstein-Barr-virus-induced mononucleosis and new-onset systemic lupus erythematosus: a case report

Distribution of granuloma

Presence of necrosis

Disease

Bronchocentric (inhalation)

Non-necrotizing

Hypersensitivity pneumonitis, lymphocytic interstitial pneumonia, talcosis

Occasionally necrotizing

Histiocytosis X

Lymphangitic

Non-necrotizing

Sarcoidosis, chronic beryllium disease

Angiocentric

Necrotizing

Wegener’s granulomatosis, lymphomatoid granulomatosis

Occasionally necrotizing

Churg-Strauss syndrome

Nodular

Necrotizing

Rheumatoid nodule