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Table 1 Classification of angioedema

From: Isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature

Hereditary

Acquired

Idiopathic

HAE-I

AAE-I

Nonhistaminergic

HAE-II

AAE-II

 

Estrogen dependent

(HAE-III)

Sex hormone dependent

 
 

Drug induced

(ACE-I, ARB)

 
  1. HAE = hereditary angioedema, AAE = acquired angioedema, ACE = angiotensin converting enzyme, ARB = angiotensin receptor blocker.