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Table 1 Previous reports of cystic fibrosis (CF) and Chiari malformation

From: Rare association between cystic fibrosis, Chiari I malformation, and hydrocephalus in a baby: a case report and review of the literature

Reference Age Sex Presenting signs and symptoms Radiologic findings (extent of Chiari, ± aqueductal stenosis, ± hydrocephalus) Treatment Follow-up Outcome
[10] 10 months M Swallowing dysfunction Not reported Chiari decompression Not reported Resolution of symptoms
[10] 18 years M Syncope Not reported Chiari decompression Not reported Resolution of symptoms
[10] 17 years F Numbness of extremities Not reported Chiari decompression Not reported Resolution of symptoms
[10] three years M Recurrent vomiting Not reported None Not reported Symptoms unresolved
[10] 17 years M Persistent headache Not reported Chiari decompression Not reported Resolution of symptoms
[13] four months M Failure to thrive Aqueductal stenosis; hydrocephalus VP shunt three months Death from sepsis
[13] eight months F Failure to thrive, nystagmus Tonsillar herniation with hydrocephalus Chiari decompression and VP shunt one year Shunt malfunction and cerebral herniation
[15] eight years F Thoracic scoliosis; gait instability; hand wasting Chiari I with thoracic scoliosis and cervicothoracic syrinx Chiari decompression two months Resolution of symptoms
Present report 10 months M Vomiting 2.2 cm of herniation; aqueductal stenosis; hydrocephalus VP shunt one month Resolution of symptoms
  1. VP = ventriculoperitoneal.