Sr No | Study | Age | T-size | IHC profile | Mol. Results | Treatment | Outcome |
---|---|---|---|---|---|---|---|
1 | Vang et al. [4] (2000) | 35 | 3 cm. | VIM+, MIC2+ | EWS/FLI1+ | WE +CT+RT | FOD (19 mo) |
2 | Farley et al. [5](2000) | 35 | 4 cm. | MIC2+ | NP | CT+EBRT+ICBT | FOD (48 mo) |
3 | Petkovic et al. [6](2002) | 45 | 9 cm. | MIC2+ | NP | CT+EBRT+ICBT | AWD (18 mo) |
4 | Liao et al. [7](2004) | 30 | 5 cm. | VIM+, MIC2+, FLI1+, synaptophysin+, neuron specific enolase (NSE)+, S-100+ | NP | TAH, BSO+ CT | FOD (36 mo) |
5 | McCluggage et al. [8] (2007) | 40 | 8 cm. | VIM+, MIC2+, FLI1- | EWS- | ∞ | ∞ |
6 | Present case (2009) | 17 | 10 cm. | VIM+, MIC2+, FLI1+, BCL2+ | EWSR1/FLI1+ | CT+Local RT | On Follow-up |