Fig. 1From: Acute fatal ventricular arrhythmia induced by severe hyperkalemia in a toddler with decompensated methylmalonic acidemiaThe metabolic pathway of methylmalonic acidemia (MMA). The accumulation of methylmalonic acid occurs owing to defects in either intracellular methylmalonyl-CoA mutase (MCM) or adenosylcobalamin, which serves as the coenzyme for MCMBack to article page